Budd
Chiari Syndrome in a Fifteen-Year Old Girl with Systemic
Lupus Erythematosus
Nageen Hussain1*, Ghazala Jaffery2,
Anjum Nasim Sabri3, Shahida Hasnain4,
Nighat Mir5
1,3,4Department
of Microbiology and Molecular Genetics, Quaid-e-Azam
Campus, University of the Punjab, Lahore-Pakistan.
2Department
of Pathology, Services Institute of Medical Sciences,
Lahore-Pakistan.
5Department
of Rheumatology, Fatimah Memorial Hospital,
Lahore-Pakistan.
*For Correspondence:
E-mail:
nageen1704@hotmail.com
International Journal of Health Research,
June
2008; 1(2):
45-49
Received: 02-Jun-08 Revision received:
06-Jun-08 Accepted for publication: 09-Jun-08
Case Report
Budd Chiari Syndrome
is a rare disease that results from the complication of
venous thrombosis. In this case report, the syndrome is
being reported in a 15 year old young Pakistani girl
first diagnosed with Systemic Lupus Erythematosus (SLE)
two years earlier. She was one of those on a one year
regular follow-up in the Rheumatology Department of
Fatimah Memorial Hospital, Lahore, Pakistan. It is
believed that in this patient, Budd Chiari Syndrome
resulted from hepatic veinous thrombosis due to the
presence of Lupus anticoagulants. As the young girl was
suffering from antiphospholipid syndrome secondary to
lupus, this milder form of Budd-Chiari Syndrome was
later treated in India with surgical shunts.
Keywords:
Systemic lupus erythematosus; Budd-Chiari Syndrome;
lupus anticoagulants; thrombosis; antiphospholipid
syndrome.
